Cardiac Amyloidosis, An Infiltrative Heart
Disease Presenting as ArrhythmiaA
Case Report
Published: April 1, 2017 | DOI: https://doi.org/10.7860/JCDR/2017/24698.9661
B Magesh, Deepak Kadeli, Sunil Bohra, V Kris hnaprasath, R Keshava
1. Junior Interventional Cardiologist, Department of Cardiology, Fortis Hospital, Bengaluru, Karnataka, India.
2. Dnb Cardiology Resident, Department of Cardiology, Fortis Hospital, Bengaluru, Karnataka, India.
3. Non Invasive Cardiologist, Department of Cardiology, Fortis Hospital, Bengaluru, Karnataka, India.
4. Dnb Cardiology Resident, Department of Cardiology, Fortis Hospital, Bengaluru, Karnataka, India.
5. Consultant Interventional Cardiologist, Department of Cardiology, Fortis Hospital, Bengaluru, Karnataka, India.
Correspondence
Dr. Deepak Kadeli,
Fortis Hospital, Cunningham Road, Bengaluru- 52, Karnataka, India.
E-mail: kadelideepak@gmail.com
Cardiac amyloidosis is a manifestation of amyloidosis which is a multisystem disorder. This is difficult to diagnose, rare disease which eventually leads to the mortality. Diagnosis requires a high index of clinical suspicion along with echocardiographic clues like, diastolic dysfunction, bi-atrial enlargement and ventricular thickening. Treatment is mainly supportive with disappointing outcomes. We present a case of systemic amyloidosis with negative congo red staining, presenting with predominantly cardiac features.
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